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Unilateral pulmonary vein atresia presenting with recurrent haemoptysis in a child: a case report

Authors
  • Wong, Martin Ngie Liong1
  • Tang, Ing Ping2
  • Chor, Yek Kee3
  • Lau, Kiew Siong3
  • John, Anne Rachel4
  • Hii, King Ching2
  • Lee, Olive Pei Yi2
  • Lim, Wooi Kok1
  • Tan, Hannah Pei Koon5
  • 1 Sarawak Heart Center, Kota Samarahan, Malaysia , Kota Samarahan (Malaysia)
  • 2 Universiti Malaysia Sarawak, Kota Samarahan, Sarawak, Malaysia , Kota Samarahan (Malaysia)
  • 3 Sarawak General Hospital, Kuching, Malaysia , Kuching (Malaysia)
  • 4 Sarawak General Hospital, Kuching, Sarawak, Malaysia , Kuching (Malaysia)
  • 5 Miri Hospital, Miri, Malaysia , Miri (Malaysia)
Type
Published Article
Journal
BMC Pediatrics
Publisher
Springer (Biomed Central Ltd.)
Publication Date
Sep 24, 2020
Volume
20
Issue
1
Identifiers
DOI: 10.1186/s12887-020-02348-7
Source
Springer Nature
Keywords
License
Green

Abstract

BackgroundHaemoptysis is an uncommon presenting symptom in children and is usually caused by acute lower respiratory tract infection or foreign body aspiration. We report a rare case of right unilateral pulmonary vein atresia (PVA) as the underlying aetiology of recurrent haemoptysis in a child.Case presentationA 4 years old girl presented with history of recurrent haemoptysis. Bronchoscopic evaluation excluded a foreign body aspiration but revealed right bronchial mucosal hyperaemia and varices. Diagnosis of right unilateral PVA was suspected on transthoracic echocardiography which demonstrated hypoplastic right pulmonary artery and non-visualization of right pulmonary veins. Final diagnosis was confirmed on cardiac CT angiography. A conservative treatment approach was opted with consideration for pneumonectomy in future when she is older.ConclusionRarer causes should be considered when investigating for recurrent haemoptysis in children. Bronchoscopy and cardiac imaging are useful tools to establish the diagnosis of unilateral PVA in our case.

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