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[Study of glycogen metabolism in the liver in type III glycogenosis (limit dextrinosis)].

Authors
  • Chibisov, I V
  • Leont'ev, A F
  • Rozenfel'd, E L
Type
Published Article
Journal
Voprosy medit︠s︡inskoĭ khimii
Publication Date
Jan 01, 1975
Volume
21
Issue
2
Pages
162–165
Identifiers
PMID: 166513
Source
Medline
License
Unknown

Abstract

Data on biochemical study of a patient with glycogenosis of the III type (limit dextrinosis) are presented. In a punctate of liver tissue absence of amylo-1,6-glucosidase activity and significant accumulation of glycogen, which was anomalous in structure, were noted. Loading with galactose and adrenaline caused alterations typical for the III type of glycogenosis. Content of glucose and lactate in blood were also studied in response to the peroral administration of glucose and protein. In erythrocytes of the patient the polysaccharide structure was shown to be anomalous; it resembled the structure of a polysaccharide from liver tissue of the patient.

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