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Staged resection for a ruptured hepatoblastoma: a 6-year follow-up

Authors
  • Madanur, Mansoor Ahmed1
  • Battula, Narendra1
  • Davenport, Mark1
  • Dhawan, Anil1
  • Rela, Mohamed1
  • 1 Kings College Hospital, Denmark Hill, London, SE5 9RS, UK , London (United Kingdom)
Type
Published Article
Journal
Pediatric Surgery International
Publisher
Springer-Verlag
Publication Date
Oct 26, 2006
Volume
23
Issue
6
Pages
609–611
Identifiers
DOI: 10.1007/s00383-006-1827-0
Source
Springer Nature
Keywords
License
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Abstract

Hepatoblastoma (HB) is a rare germ cell tumour of childhood usually presenting with progressive abdominal distention. However, presentation as acute abdomen is a rare occurrence and is secondary to spontaneous rupture. This presentation carries high mortality. To our knowledge, six cases of ruptured hepatoblastoma have previously been reported, although the long-term outcome has not been clear. We report a case of ruptured HB who was managed by initial control of haemorrhage by laparotomy followed by chemotherapy with high-risk hepatoblastoma protocol as per SIOPEL 2 (cisplatin, carboplatin and doxorubicin) and a staged hepatectomy 5 months later. Patient is currently disease free at 6-year follow-up. Staged hepatectomy after initial control of haemorrhage does not preclude a curative resection.

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