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Severe hemorrhage complicating the Klippel-Trénaunay-Weber syndrome.

Authors
  • Aronoff, D M
  • Roshon, M
Type
Published Article
Journal
Southern medical journal
Publication Date
Nov 01, 1998
Volume
91
Issue
11
Pages
1073–1075
Identifiers
PMID: 9824196
Source
Medline
License
Unknown

Abstract

The Klippel-Trénaunay-Weber (KTW) syndrome is a congenital disorder of angiogenesis characterized by macular nevus, skeletal and soft tissue hypertrophy, venous varicosities, and arteriovenous fistulas. Disseminated intravascular coagulation (DIC) and the Kasabach-Merritt syndrome, a consumptive coagulopathy with thrombocytopenia, are both associated with the KTW syndrome. We describe a 30-year-old woman with KTW syndrome and Kasabach-Merritt syndrome who had DIC with severe hemorrhage after a routine gynecologic procedure. The bleeding was controlled with the use of intravenous low-dose heparin and antithrombin III.

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