Affordable Access

Pulmonary hypertension associated with primary biliary cirrhosis in the absence of portal hypertension: a case report.

Authors
  • E M Yoshida
  • S R Erb
  • D N Ostrow
  • D R Ricci
  • C H Scudamore
  • G Fradet
Publication Date
Feb 01, 1994
Source
PMC
Keywords
Disciplines
  • Medicine
License
Unknown

Abstract

Pulmonary hypertension is well described in association with portal hypertension of any cause including end stage primary biliary cirrhosis (PBC). The essential feature of this association is the presence of portosystemic shunting, including surgically created shunts. A patient with primary pulmonary hypertension and PBC without portal hypertension is reported. This suggests that primary pulmonary hypertension may be associated with PBC in the absence of portal hypertension. Decisions regarding appropriate organ transplantation may depend on whether pulmonary hypertension is primary or secondary to portal hypertension.

Report this publication

Statistics

Seen <100 times