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Progressive unilateral encephalopathy of childhood (Rasmussen's syndrome): a reappraisal.

Authors
  • Vining, E P
  • Freeman, J M
  • Brandt, J
  • Carson, B S
  • Uematsu, S
Type
Published Article
Journal
Epilepsia
Publication Date
Jan 01, 1993
Volume
34
Issue
4
Pages
639–650
Identifiers
PMID: 8330574
Source
Medline
License
Unknown

Abstract

Twelve children with Rasmussen's encephalitis underwent hemispherectomy and have been followed for an average of 9.15 years. Our decision-making process leads to early, rather than late operation. Because hemiplegia is inevitable with or without operation, earlier operation may allow such children to resume a more normal life. We postulate that earlier operation may prevent some of the intellectual decline that accompanies the continued seizures and their treatment. In view of the variable pathologic findings and lack of evidence of a viral etiology, we suggest either use of the term "progressive unilateral encephalopathy of childhood" or "Rasmussen's syndrome" in recognition of its heritage.

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