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Progressive facial hemiatrophy: central nervous system involvement and relationship with scleroderma en coup de sabre.

Authors
  • Blaszczyk, Maria
  • Królicki, Leszek
  • Krasu, Mateusz
  • Glinska, Olga
  • Jablonska, Stefania
Type
Published Article
Journal
The Journal of rheumatology
Publication Date
Sep 01, 2003
Volume
30
Issue
9
Pages
1997–2004
Identifiers
PMID: 12966605
Source
Medline
License
Unknown

Abstract

Our results suggest frequent CNS involvement in PFH cases, regardless of the time of presentation of cutaneous indurations, with or without coexistent plaques of localized scleroderma in other locations. This indicates a close relationship between PFH and scleroderma en coup de sabre. The detection of abnormal SPECT by normal MRI in some cases of PFH and scleroderma en coup de sabre is of practical importance. This indicates the usefulness of SPECT in studying both PFH and scleroderma en coup de sabre.

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