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Lymphangiomyomatosis: a respiratory illness with an endocrinologic therapy.

Authors
  • Sieker, H O
  • McCarty, K S Jr
Type
Published Article
Journal
Transactions of the American Clinical and Climatological Association
Publication Date
Jan 01, 1988
Volume
99
Pages
57–67
Identifiers
PMID: 3503438
Source
Medline
License
Unknown

Abstract

Lymphangiomyomatosis should be considered when unexplained dyspnea, pneumothorax, pleural effusion or infiltrative radiographic changes occurs in a woman of childbearing age. Radiographic and pulmonary function peculiarities help in the diagnosis and evaluation of results of treatment. Diagnosis is dependent on lung biopsy and preferably identification of hormonal receptors. Endocrinological manipulation, in this study with medroxyprogesterone, decreased disability, morbidity and progression of this otherwise fatal illness. Early diagnosis and institution of treatment would appear to provide the best result.

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