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Hereditary spinal arachnoid cysts, distichiasis, and lymphedema.

Authors
  • Schwartz, J F
  • O'Brien, M S
  • Hoffman, J C Jr
Type
Published Article
Journal
Annals of neurology
Publication Date
Apr 01, 1980
Volume
7
Issue
4
Pages
340–343
Identifiers
PMID: 7377759
Source
Medline
License
Unknown

Abstract

Familial congenital spinal arachnoid cysts causing progressive paraplegia are reported in two adolescent siblings as part of a hereditary syndrome. The other features of this unusual dominantly inherited disorder include double rows of eyelashes, partial ectropion of the lower eyelids, and acquired late-onset lymphedema of the lower extremities. The siblings' mother, who had roentgenographic evidence of a similar intraspinal lesion, was free of neurological symptoms but had the other characteristic features. Surgical treatment of the arachnoid cysts improves the progressive paraplegia.

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