Abstract Open surgery is the standard therapeutic approach for renal malignant tumor in children; while in adults, laparoscopic radical nephrectomy (LRN) is used. Only few reports on LRN in children have been published because the most common form of pediatric renal malignancy, Wilms tumor, is well known for presenting with large palpable masses. Here, we report the case of a 13-year-old girl with small chromophobe renal cell carcinoma (RCC) who was managed by LRN. RCC is a rare condition, with an incidence rate of only 2–6% of all renal tumors in children. We found LRN for small RCC to be feasible and safe.