Affordable Access

Fatal primary pulmonary hypertension in mixed connective tissue disease.

Authors
  • Eulderink, F
  • Cats, A
Type
Published Article
Journal
Zeitschrift für Rheumatologie
Publication Date
Jan 01, 1981
Volume
40
Issue
1
Pages
25–29
Identifiers
PMID: 7223079
Source
Medline
License
Unknown

Abstract

The clinical history and autopsy findings are reported of a 23 year old woman who had symptoms of mixed connective tissue disease (MCTD) for 4 years, and who died suddenly from pulmonary hypertension due to proliferative endarteritis of the lung vessels. These arterial lesions resembled those in progressive systemic sclerosis. Children and adolescents with MCTD appear to have an increased risk for getting this complication. The fatal outcome of pulmonary hypertension in MCTD as shown in this and other cases seems to warrant treatment with immunosuppressive drugs.

Report this publication

Statistics

Seen <100 times