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Chronic Refractory Uveitis in a Patient with Childhood-Onset Cyclic Neutropenia

Authors
Journal
Case Reports in Ophthalmology
1663-2699
Publisher
S. Karger AG
Publication Date
Volume
2
Issue
2
Identifiers
DOI: 10.1159/000328748
Source
Legacy
Keywords
  • Published: May 2011
Disciplines
  • Medicine

Abstract

We report a rare case of chronic refractory uveitis in a patient with childhood-onset cyclic neutropenia (CN). A 19-year-old woman, who had a history of CN beginning at age 2, presented with bilateral chronic nongranulomatous uveitis, complicated cataract, retinal vasculitis, cystoids macular edema, and vitreous hemorrhage. She had recurrent episodes of oral ulcers, tonsillitis, genital ulcers, and folliculitis during neutropenic nadir. After the resumption of granulocyte colony-stimulating factor therapy for her CN, vitreous hemorrhage in both eyes followed. Her eyes were treated with topical corticosteroids, retinal photocoagulation, and cataract surgery. Blood and bone marrow test results confirmed the diagnosis of CN. She also fulfilled the diagnostic criteria of Behçet's disease, though clinical features of her uveitis were dissimilar to those found in that disease.

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