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[A case of pheochromocytoma with von Recklinghausen's and review of 67 Japanese cases].

Authors
Type
Published Article
Journal
Nihon Hinyōkika Gakkai zasshi. The japanese journal of urology
Publication Date
Volume
92
Issue
3
Pages
479–483
Identifiers
PMID: 11398324
Source
Medline
License
Unknown

Abstract

A 19-year-old woman with von Recklinghausen's disease was referred to our hospital because of right adrenal pheochromocytoma. The tumor was detected incidentally with the abdominal ultrasonography when she complained epigastralgia to the home doctor who treated her hypertension. Plasma and urinary catecholamines level were elevated. The tumor was removed by laparoscopy assisted adrenalectomy without pneumoperitoneum. The resected specimen was 35 x 60 x 75 mm in size and weighed 70 g. Pathological diagnosis was adrenomedullary pheochromocytoma. Postoperative course was uneventful. She has been well with no signs of recurrence after 7.5 years. We reviewed 67 Japanese patients previously reported as von Recklinghusen's disease with pheochromocytoma. Of the 60 patients whose details were described, 16.7% had metastases and pathological malignancy from pheochromocytoma.

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