Affordable Access

Acute Pancreatitis with Rapid Clinical Improvement in a Child with Isovaleric Acidemia

Authors
Publisher
Case Reports in Pediatrics
Publication Date
Disciplines
  • Medicine

Abstract

Isovaleric acidemia is a rare branched-chain organic acidemia. The authors describe a 3.5-year-old girl with isovaleric acidemia and acute abdominal pain associated with bilious emesis. Elevated serum amylase and abdominal ultrasonography demonstrating an enlarged and edematous pancreas, along with the presence of peripancreatic exudates, confirmed the presence of acute pancreatitis. The patient recovered quickly with intravenous hydration, pancreatic rest, and administration of intravenous L-carnitine. Pancreatitis should be ruled out in the context of vomiting in any patient with isovaleric acidemia. Conversely, branched-chain organic acidemias should be included in the differential diagnosis of any child with pancreatitis of unknown origin.

There are no comments yet on this publication. Be the first to share your thoughts.

Statistics

Seen <100 times
0 Comments

More articles like this

Acute Pancreatitis with Rapid Clinical Improvement...

on Case Reports in Pediatrics Jan 01, 2013

[Isovaleric acidemia].

on Ugeskrift for laeger Nov 26, 1979

[Acidemia, isovaleric].

on Ryōikibetsu shōkōgun shirī... 2001
More articles like this..