We report a case of a rare type of bronchoesophageal fistula that communicated with the patient's normal bronchial tree, but had systemic arterial supply. Although included within the spectrum of bronchopulmonary foregut malformations, only three other similar cases have been reported in the literature. At the time of presentation, the 11-month-old male patient was afebrile with coarse breath sounds at the left lung base. A barium swallow demonstrated the connection between the distal esophagus and a left lower lobe bronchus. CT also helped to delineate the course of the fistula.