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Aqueductal stenosis in neurofibromatosis.

Authors
  • Riviello, J J Jr
  • Marks, H G
  • Lee, M S
  • Mandell, G A
Type
Published Article
Journal
Neurofibromatosis
Publication Date
Jan 01, 1988
Volume
1
Issue
5-6
Pages
312–317
Identifiers
PMID: 3152484
Source
Medline
License
Unknown

Abstract

Macrocrania (i.e., macrocephaly) is a common manifestation of von Recklinghausen neurofibromatosis (NF-1), occurring in approximately 30% of patients with this disorder. Megalencephaly is the usual basis for NF-1-associated macrocrania, although obstructive hydrocephalus secondary to a brain tumor or cranial vault dysplasia may occur. We describe 2 patients with NF-1 and aqueductal stenosis documented by CT scan. The incidence of aqueductal stenosis among our patients with NF-1 is 1%.

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