Affordable Access

Aplasia of the right aortic cusp in a neonate: a life-threatening but curable anomaly.

Authors
  • Henze, A C
  • Malm, T K
  • Sunnegårdh, J T
  • Hallberg, M B
Type
Published Article
Journal
The Annals of Thoracic Surgery
Publisher
Elsevier
Publication Date
Dec 01, 1991
Volume
52
Issue
6
Pages
1329–1330
Identifiers
PMID: 1755689
Source
Medline
License
Unknown

Abstract

A case of absent right aortic cusp causing serious aortic incompetence in a neonate is reported. A "bicuspidalization" repair broke down within 24 hours, but reoperation with annular enlargement and insertion of a 19-mm prosthetic valve resulted in complete recovery. This rare but life-threatening anomaly of the aortic valve can be recognized with Doppler echocardiography. Valve replacement in conjunction with aortic annular enlargement should be performed as primary repair.

Report this publication

Statistics

Seen <100 times