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Aplasia of the right aortic cusp in a neonate: a life-threatening but curable anomaly.

Authors
Type
Published Article
Journal
The Annals of Thoracic Surgery
0003-4975
Publisher
Elsevier
Publication Date
Volume
52
Issue
6
Pages
1329–1330
Identifiers
PMID: 1755689
Source
Medline
License
Unknown

Abstract

A case of absent right aortic cusp causing serious aortic incompetence in a neonate is reported. A "bicuspidalization" repair broke down within 24 hours, but reoperation with annular enlargement and insertion of a 19-mm prosthetic valve resulted in complete recovery. This rare but life-threatening anomaly of the aortic valve can be recognized with Doppler echocardiography. Valve replacement in conjunction with aortic annular enlargement should be performed as primary repair.

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