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Aorticopulmonary paraganglioma and gastric leiomyoblastoma in a young woman.

Authors
  • Grace, M P
  • Batist, G
  • Grace, W R
  • Gillooley, J F
Type
Published Article
Journal
The American Journal of Medicine
Publisher
Elsevier
Publication Date
Jun 01, 1981
Volume
70
Issue
6
Pages
1288–1292
Identifiers
PMID: 6263093
Source
Medline
License
Unknown

Abstract

The 16th report of a patient with "Carney's triad" is presented. The triad consists of an extra-adrenal paraganglioma, gastric leiomyoblastomas and a pulmonary chondroma. The diagnosis is made by discovery of the presence of at least two of these individually rare tumors. The patient described as 15 year old girl who presented with a pericardial effusion caused by an invasive mediastinal paraganglioma. She was subsequently found to have multiple gastric leiomyoblastomas. The leiomyoblastomas have been resected. The paraganglioma was unresectable, and the patient underwent sequential radiation therapy and chemotherapy without response. Concomitant 5-fluorouracil chemotherapy with radiation resulted in an objective regression of tumor mass.

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