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Absent pulmonary valve, intact interventricular septum, rudimentary aortic non-coronary cusp and ascending aortic aneurysm in a single patient.

Authors
Type
Published Article
Journal
Interactive Cardiovascular and Thoracic Surgery
1569-9285
Publisher
Oxford University Press
Publication Date
Volume
10
Issue
4
Pages
636–638
Identifiers
DOI: 10.1510/icvts.2009.225508
PMID: 20118119
Source
Medline
License
Unknown

Abstract

Absent pulmonary valve (APV) is a relatively rare congenital heart disease, and is mostly associated with tetralogy of Fallot phenotype or ventricular septal defect. APV with intact interventricular septum (IVS) is even less common with case reports or very small series in the literature. Congenital aortic regurgitation with a rudimentary non-coronary cusp is also by itself a rare congenital anomaly and to our knowledge this is the first report of the combination of APV, intact IVS, abnormal aortic valve and ascending aortic aneurysm. The clinical course, possible etiologies and management are discussed.

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