Background Cutaneous disorders can be associated with a wide variety of dental manifestations that should be familiar to dermatologists. Objective We sought to describe the development of the teeth, explain current dental terms, and review the dental manifestations of some dermatologic conditions. Methods A MEDLINE search (1966-May 2007) was performed to find relevant articles pertaining to dental manifestations of dermatologic conditions. Results Dental manifestations are associated with a wide variety of skin diseases that include genetic, infectious, inflammatory, and immune disorders. Limitations The review is broad and focuses on commonly described manifestations. Conclusions An appreciation and understanding of dental signs can aid in the diagnosis and treatment of many skin conditions.