Summary Congenital sarcoma is a rare lesion. A case of congenital sarcoma of the foot is reported. Analysis of all reported cases shows that congenital sarcoma of the extremities has a surprisingly good prognosis. Treatment is surgical. Amputation at the lowest possible level appears to be the most sensible approach. Radiation is no substitute for surgery but its possibilities cannot be fairly judged at this time. Congenital sarcoma in locations other than the extremities has a much graver prognosis. Surgical treatment is usually impractical or ineffective. Radiotherapy is considered preferable in this group whenever complete removal is impossible.